2024/12/31 by N Kasdallah., H BenSalem, H Kbaier +4
#Child #Congenitalcysticadenomatoidmalformation #Malformationadénomatoïdekystiquepulmonaire #Newborn #enfant #nouveau-né #prenatalultrasoundscreening #échographieanténatale
paper · doi:10.71566/pist-rmp-194892
Introduction : Congenital cystic adenomatoid malformations (CCAM) are congenital abnormalities of lungdevelopment. Theyrepresentapproximately25%ofcongenitallungdiseases. WhenCCAMaresymp- tomatic,respiratorydistressoftenoccursduringtheneonatalperiod. Thediagnosisismadein80to85% ofcasesbeforetheageoftwoyearsfollowingrespiratoryinfections. Results:We reportthree cases ofCCAM includingtwo cases inwhich prenatal diagnosiswas made. One of the patients didn’t present any respiratory symptoms and the diagnosis was fortuitous. The CCAM was associated with hyaline membrane disease in one case of aterm newborn and with transient tachypnea inapremature baby. The CCAMwas situated in the right lung in all cases. Histological examination based on Stockerclassification confirmedthe diagnosis oftype I CCAM intwo cases andtype II in one case. Allthree patients had beneficed of surgery with a favorable evolution. Conslusion:TheperinatalcareofCCAMhasimprovedsignificantlythankstoprenatalultrasoundscree- ning especially in severe forms. The other causes of neonatal respiratory distress can make the diagnosis difficult. The most frequent complications are neonatal respiratorydistress and recurrent chest infections. Surgery remains the indicated treatment for symptomatic forms.