2024/12/31 by Tilouche, S., Bouguila J, Boughamoura L +4
#Congenital cystic adenomatoid mal- formation #Pneumothorax #child #enfant #malformationadénomatoïde kys- tiquedupoumon
paper · doi:10.71566/pist-rmp-194946
Introduction:Congenitalcysticadenomatoidmalformationisthemostcommoncongenitallunglesion. Spontaneouspneumothorax, asthe initial manifestation ofcongenitalcystic adenomatoid malformation, is rare and few cases have been described in the literature. Purpose:Wereportacaseofthisdiseaseinachildwhopresentedwithfeaturesofpneumothorax Casepresentation:Atenyearoldboyhadaseven day history of onset of breathlessness and pain in the left side of the chest. The child had tachypnea with a tympanic note on percussion and decreased breath sounds on the left hemithorax. An urgent chest X-ray revealed a large pneumothorax with collapsedleftlung. Fewcysticlesionswerenoted in the left lung. A needle aspiration was done. A computed tomography scan of chest showed re- currence of the pneumothorax, cutaneous emphy- sema and demonstrated a large well defined cap- sulated and thin walled cavity occupying left lower lobe. A second needle aspiration chest was put to drain the air. A lobectomy was done. The histologi- cal study confirmed the diagnosis of type I cystic adenomatoidmalformationofthelung. Conclusion: clinicians should be aware ofthe pos- sibility that spontaneous pneumothorax may be the initial presentation of CCAM in children. They should undergo appropriate imaging studies to diagnose thismalformation