2024/09/13 by Andrei Galafton, Ronny R. Buechel, Fran Mikulicic +2 · 1 voice
Medicine · #Sarcoidosis and Beryllium Toxicity Research #Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis #Vasculitis and related conditions
paper · pdf · doi:10.1007/s10554-024-03232-6
openalex publication_date 2024/09/13 · openalex created_date 2025/10/10 · openalex updated_date 2026/08/03
Cardiac sarcoidosis is a rare form of systemic sarcoidosis characterized by formation of non-caseating granulomas in the myocardium, leading to heterogeneous manifestations, including conduction disturbances, arrhythmias, and heart failure. Besides myocardial fibrosis and structural myocardial alterations, cardiac sarcoidosis can impact the epicardial and microvascular circulation, causing ischemia and regional microvascular dysfunction. We present a case of cardiac sarcoidosis with atypical initial presentation but with evidence of disease in myocardial perfusion imaging, which was overlooked since it did not correspond to bystander coronary artery disease. Multimodality imaging facilitated diagnosis and offered insights into the regional microcirculation impairment caused by sarcoidosis-induced inflammation.