Fibrillin-Related Proteins Control Calcium Homeostasis in Dystrophic Muscle Across Species

2025/06/16 by Damiano Marchiafava, Andres Vidal Gadea
Biochemistry, Genetics and Molecular Biology · Medicine · #Muscle Physiology and Disorders #Adipose Tissue and Metabolism #Cardiomyopathy and Myosin Studies

paper · doi:10.17912/micropub.biology.001697

Abstract

. These findings identify fibrillin-related proteins as potential regulators of muscle calcium homeostasis across species and suggest that ECM-calcium coupling represents a conserved pathological mechanism in muscular dystrophy.

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